Pulmonary Malformations

General

• Variety of tissue or vascular anomalies

•  Presentation varies from life threatening to asymptomatic

•  Age of onset depends on severity of lesion

•  Long term complications typically related to degree of lung impairment (pulmonary hypoplasia)

Malformation, Presentation, Age of Onset, Imaging

Laryngomalacia

1. Stridor

2. Late infancy

3. Endoscopy

Vascular rings/slings

1. stridor or feeding issues

2. varies

3. barium swallow or CT/MRI

TE Fistula

1. feeding issues or recurrent pneumonia

2. varies

3. contrast study or bronchoscopy

Pulmonary Sequestration

1. recurrent PNA

2. varies

3. CXR then CT

CLE (Congenital Lobar Emphysema)

1. Resp distress

2. late infancy

3. CXR

Bronchogenic cyst

1. resp distress

2. varies

3. CXR +/- CT

CCAM

1. same as bronchogenic cyst

Congenital Diaphragmatic Hernia

1. resp distress

2. delivery

3. CXR